Abstract: Orbital solitary fibrous tumor (SFT) is a rare tumor originating from perivascular multipotent mesenchyme and can occur in various parts of the orbit. Mass involving in the orbit and proptosis are the most common manifestations. The age of onset is 40-50 at most and there is no difference in incidence between men and women. A small percentage of orbital SFT patients may experience tumor recurrence and metastasis. The clinical and imaging findings of orbital SFT are mostly non-specific. The histopathological morphologic changes of orbital SFT are extensive and there are many subtypes. Immunohistochemical staining has high specificity. Surgical resection is the main treatment for orbital SFT, and close follow-up is very important. (Int Rev Ophthalmol, 2022, 46:  378-384)

Key words: orbital, solitary fibrous tumor