Abstract: Congenital cataract is  developed due to the metabolic disturbance of lens in embryo, which induces the degression of the transparency of lens. Genetic factors are associated with development of this disease. Autosomal dominant congenital cataract （ADCC） is the major type in reported congenital cataract. So far, twentytwo genes associated with ADCC have been found. These genes invole CRY, GJA, MIP, BFSP, transcription factor, and so on. This paper summarizes the genetic researches on ADCC in recent years.